Trifid Cord; Very Rare Presentation of Split Cord Malformation
نویسندگان
چکیده
A child with a very rare anomaly of spinal cord is described. The patient presented at 9 months of age with trifid cord at thoracolumbar region and extensive split cord malformation (SCM) from T12-L5. She had a composite type SCM including type II at T12-L1 and SCM type I from L2, L3, to L4 levels. The condition seemed to be something like three distinct cords at T12-L1 level composed of a thin cord at left side terminating before L2 level to a tiny fibrous band, and two thick middle and right cords which joined together at conus at L5 level. The patient had a large hairy patch on her back with asymmetric legs without any movements in her smaller foot. Cord untethering and removing the bony ridge causing SCM were performed with laminectomy of L2 to L5 and laminotomy of T12 and L1, Her neurological status was unchanged after surgery and remained stable during 6 month follow up.
منابع مشابه
Spondylocostal dysostosis associated with type I split cord malformation and double nipple on one side: a case report.
Jarcho Levin syndrome is a rare genetic disorder characterized by multipl vertebral and costal anomalies at birth. Jarcho Levin syndrome includes two phenotypic groups: spondylothoracic dysostosis and spondylocostal dysostosis. The prognosis of spondylothoracic dysostosis has worse than spondylocostal dysostosis, because of respiratory complications. Associated malformations include those of th...
متن کاملLong segment composite split cord malformation with double bony spur
A composite type of SCM is very rare and only a few cases have been reported until today. The frequency of compositetype SCM is lower than 1% in the literature. In this report, we presented an unusual case of long segment composite type split cord malformation with double level bony spur with multiple associated bony anomalies.
متن کاملComposite type of split cord malformation: rare and difficult to explain.
do different types of malformations occur at different levels? The multiple canal theory is not a reasonable and satisfactory enough option to explain the development of such a malformation. Although the cellular mechanisms responsible for such a theory are not fully known, experimentally induced perturbations of Hensen’s node and the primitive streak during gastrulation have resulted in embryo...
متن کاملType I Split Spinal Cord Malformation: Literature review, Case presentation and Surgical Technique
Background: Split Spinal cord Malformation (SSCM) is a form of spinal dysraphism in which any or all of the spinal cord, cauda equina, and filum terminale are divided by a bony or fibrous spur. There are two described types of SSCM, namely Types I and II. In Type I SSCM, there are separate hemi-cords contained in two dural sacs, separated by a bony spur; in Type II SSCM, there is a single dural...
متن کاملWell differentiated liposarcoma of spermatic cord: report of 3 rare cases
Spermatic cord liposarcomas are very rare tumors. Patients usually present with painless growing scrotal swellings which are clinically misdiagnosed as hernia. The correct diagnosis is not common and usually they present as operative or histological surprises. To our knowledge, there are about 186 similar cases reported in the literature. Herein we report three cases of spermatic cord li...
متن کامل